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 > 西医科室 > 内科 > 血液内科
百科

δ-贮存池病

血液科

Common symptoms

牙龈出血、月经量多、鼻出血

The pathology of disease

δ-贮存池病(δ-storagepooldisease,δ-SPD)由Weiss等于1969年首先描述,本病是一种异质性疾病,以患者有轻度出血倾向,血小板第二相聚集波异常,血小板致密体可有不同程度减少为特征。

常见症状

牙龈出血;月经量多;鼻出血

发病病因

(一)发病原因 目前暂无相关资料 (二)发病机制 基本缺陷是血小板致密颗粒内容物ADP,ATP,5-羟色胺,钙离子等均减少。

治疗方式

药物治疗、支持性治疗

预防措施

δ-贮存池病日常预防 遗传方式未明,但已发现有些患者呈常染色体显性遗传。

就诊科室

建议前往血液科就诊,就诊前可先通过本平台预约挂号与专家对接。

温馨提示:以上信息仅供健康科普参考,不能替代专业医疗诊断。如有相关症状请及时到正规医院就诊。