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Home > West Medicine > ENT & Ophthalmology > Ophthalmology
L12.100

Cicatricial Pemphigoid

眼科

Common symptoms

受伤后易产生瘢痕、蹼状瘢痕、角膜溃疡、耳孔处长出的肿物、眼结膜水肿及角膜溃疡、角膜大小不等的...

The pathology of disease

Cicatricial (mucous-membrane) pemphigoid is autoimmune subepidermal blistering with scarring of mucosa (ocular/oral/genital/laryngeal/esophageal), presenting with ocular conjunctival erosions, symblepharon, and potential blindness. Treatment: systemic corticosteroids; steroid-sparing agents (dapsone/azathioprine/mycophenolate/methotrexate); rituximab/cyclophosphamide for severe ocular; IVIG; ophthalmology/ENT/dental care; ocular surgery for symblepharon; monitor airway/vision; follow-up.

Common Symptoms

Mucosal erosions; scarring; symblepharon; ocular/oral/genital

Causes and Pathogenesis

Anti-BP180/laminin-332 antibodies cause subepidermal split and mucosal scarring.

Treatment

Steroids; dapsone/steroid-sparing; rituximab; ocular/ENT/dental care

Preventive Measures

Early ophthalmology/ENT care; monitor vision/airway.

Department to Visit

It is recommended to visit the Dermatology/Ophthalmology/ENT/Oral-medicine department; an appointment can be booked on this platform before the visit.

Warm reminder: The above information is for health science reference only and cannot replace professional medical diagnosis. If you have related symptoms, please seek medical attention at a regular hospital promptly.