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Home > West Medicine > OB-GYN > Gynecology
百科

Alveolar soft part sarcoma of vulva

妇科

Common symptoms

大阴唇或肛门大...

The pathology of disease

Alveolar soft part sarcoma of vulva is rare slow-growing vascular sarcoma; young women; ASPSCR1-TFE3; late lung/brain mets; surgery; anti-angiogenic.

Symptoms

Slow vulvar mass; young women; vascular; late lung/brain metastases; indolent but malignant

Causes

ASPSCR1-TFE3 translocation; rare sarcoma.

Treatment

Wide surgical excision; anti-angiogenic (pazopanib); surveillance for lung/brain mets; oncology

Dept

Oncology / gynecology / dermatology.

Warm reminder: Health education reference only; seek care at regular hospital.