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Home > West Medicine > Pediatrics > Pediatric Internal Med
百科

Acrodermatitis enteropathica

小儿内科

Common symptoms

疱疹、官爵银、腹泻、脓疱、口腔溃疡、舌炎、脱发、指(趾)甲缺失

The pathology of disease

Acrodermatitis enteropathica is zinc malabsorption (ZIP4); periorificial/acral dermatitis; diarrhea; alopecia; infants; oral zinc lifelong.

Symptoms

Periorificial/acral dermatitis; diarrhea; alopecia; irritability; infant; after weaning; zinc-responsive

Causes

ZIP4 mutation; zinc malabsorption; autosomal recessive; acrodermatitis enteropathica.

Treatment

Oral zinc supplementation lifelong; diet; dermatology/metabolic; genetic counseling

Dept

Dermatology / pediatrics / metabolic / genetics.

Warm reminder: Health education reference only; seek care at regular hospital.