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Home > West Medicine > Pediatrics > Pediatric Internal Med
百科

Wegener granulomatosis in children (GPA)

儿科综合

Common symptoms

鼻黏膜溃疡、胸痛、血尿、瘀斑、鼻塞、气短、眼睑下垂、葡萄膜炎、运动失调、感觉障碍

The pathology of disease

Wegener granulomatosis in children (granulomatosis with polyangiitis) is small-vessel vasculitis; upper/lower respiratory; kidney; c-ANCA; children; children; steroids/immunosuppression; pediatric rheumatology.

Symptoms

Sinus; cough; hemoptysis; glomerulonephritis; child; c-ANCA; steroids/immunosuppression

Causes

Small-vessel vasculitis; ANCA; GPA; child.

Treatment

Steroids; rituximab/cyclophosphamide; maintenance; pediatric rheumatology; long-term

Dept

Pediatric rheumatology / pediatric nephrology / pediatrics.

Warm reminder: Health education reference only; seek care at regular hospital.