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 > West Medicine > Other Specialties > Oncology
百科

Vulvar epithelioid sarcoma

肿瘤外科

Common symptoms

大阴唇或肛门大...、结节

The pathology of disease

Vulvar epithelioid sarcoma is rare slow-growing nodular sarcoma; young women; distal extremities typical but vulvar occurs; INI1 loss; surgery; aggressive.

Symptoms

Slow vulvar nodules; young women; ulceration; recurrence; regional nodes; biopsy; INI1 loss

Causes

Epithelioid sarcoma; INI1 (SMARCB1) loss; rare.

Treatment

Wide surgical excision; sentinel node; chemotherapy/radiation for advanced; oncology follow-up

Dept

Oncology / gynecology / dermatology.

Warm reminder: Health education reference only; seek care at regular hospital.