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Home > West Medicine > Internal Medicine > Respiratory Medicine
百科

Immotile cilia syndrome

呼吸内科

Common symptoms

中耳和耳咽管纤毛异常、呼吸困难、咯血、肺不张、脓痰、纤毛结构缺陷、脓性分泌物

The pathology of disease

Immotile cilia syndrome (primary ciliary dyskinesia) is ciliary dyskinesia; chronic sinusitis/otitis; bronchiectasis; situs inversus; male infertility; airway clearance.

Symptoms

Chronic cough; recurrent sinusitis/otitis; bronchiectasis; neonatal distress; situs inversus; male infertility

Causes

Ciliary dynein arm defect; autosomal recessive; impaired mucociliary clearance.

Treatment

Airway clearance; antibiotics; treat sinus/otitis; fertility; pulmonology; genetics

Dept

Pulmonology / ENT / pediatrics / genetics.

Warm reminder: Health education reference only; seek care at regular hospital.