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Home > West Medicine > Internal Medicine > Hematology
百科

Microscopic polyangiitis

血液科

Common symptoms

官爵银、呼吸困难、肌痛、咯血、口腔溃疡、腹痛、肾病综合征、少尿、蛋白尿

The pathology of disease

Microscopic polyangiitis is p-ANCA (MPO) small-vessel vasculitis; pauci-immune glomerulonephritis; pulmonary capillaritis; no granulomas; rituximab/cyclophosphamide.

Symptoms

Hematuria/renal failure; hemoptysis; purpura; fever/weight loss; p-ANCA; no sinus granulomas; older

Causes

MPO-ANCA; small-vessel vasculitis; no granulomas (distinguishes GPA).

Treatment

Rituximab/cyclophosphamide + steroids; maintenance; renal/pulmonary monitoring; rheumatology

Dept

Rheumatology / nephrology / pulmonology.

Warm reminder: Health education reference only; seek care at regular hospital.